The Japanese clinical guidelines 2022 for myasthenia gravis and Lambert–Eaton myasthenic syndrome

نویسندگان

چکیده

The revised Japanese clinical guidelines for myasthenia gravis (MG) and Lambert–Eaton myasthenic syndrome (LEMS) were published in 2022. notable points these (GLs) are as follows: (i) the first GLs to include a description of LEMS; (ii) diagnostic criteria MG lessen incidence false negative patients; (iii) is divided into six subtypes; (iv) high-dose oral steroid regimen with escalation de-escalation schedule not recommended by GLs; (v) promote early fast-acting treatment strategy initially proposed previous (vi) refractory defined; (vii) use molecular targeted drugs included; (viii) LEMS proposed; (ix) algorithms both presented. These new expected improve patients' quality life will serve bridge present era eras.

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ژورنال

عنوان ژورنال: Clinical and Experimental Neuroimmunology

سال: 2023

ISSN: ['1759-1961']

DOI: https://doi.org/10.1111/cen3.12739